{"code":"C85014","name":"Pityriasis Rubra Pilaris","terminology":"ncit","version":"26.10d","conceptStatus":"DEFAULT","leaf":true,"active":true,"synonyms":[{"name":"Pityriasis Rubra Pilaris","termType":"PT","type":"FULL_SYN","typeCode":"P90","source":"NCI"},{"name":"Pityriasis Rubra Pilaris","type":"Preferred_Name","typeCode":"P108"}],"definitions":[{"definition":"A rare cutaneous disorder of unknown etiology characterized by the presence of reddish-orange scaly plaques, palmoplantar keratoderma, keratotic follicular papules, and confluent erythematous areas with areas of normal skin between the lesions.","code":"P97","type":"DEFINITION","source":"NCI"}],"properties":[{"code":"P106","type":"Semantic_Type","value":"Disease or Syndrome"},{"code":"P207","type":"UMLS_CUI","value":"C0032027"}],"parents":[{"code":"C27555","name":"Non-Neoplastic Skin Disorder"},{"code":"C53543","name":"Rare Non-Neoplastic Disorder"}],"roles":[{"code":"R108","type":"Disease_Has_Finding","relatedCode":"C39570","relatedName":"Cutaneous Involvement"},{"code":"R100","type":"Disease_Has_Associated_Anatomic_Site","relatedCode":"C12907","relatedName":"Integumentary System"},{"code":"R108","type":"Disease_Has_Finding","relatedCode":"C42094","relatedName":"Rare Lesion"},{"code":"R101","type":"Disease_Has_Primary_Anatomic_Site","relatedCode":"C12470","relatedName":"Skin"}]}